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Table 1 Vasculitis entities eligible for inclusion in the GeVas registry

From: The Joint Vasculitis Registry in German-speaking countries (GeVas) – a prospective, multicenter registry for the follow-up of long-term outcomes in vasculitis

Vasculitis entities

1. Large vessel vasculitis

 • Giant Cell Arteritis

 • Takayasu Arteritis

2. Medium size vessel vasculitis

 • Polyarteritis nodosa

 • Kawasaki disease

3. Small vessel vasculitis

ANCA-associated vasculitides

  • Microscopic Polyangiitis

  • Granulomatosis with Polyangiitis

  • Eosinophilic Granulomatosis with Polyangiitis

Immune complex vasculitis

  • Anti-GBM(glomerular basement membrane) disease

  • Cryoglobulinemic vasculitis

  • IgA vasculitis

  • Hypocomplementemic urticarial vasculitis (Anti-C1q vasculitis)

4. Variable Vessel Vasculitis

 • Behcet’s disease

 • Cogan’s Syndrome

5. Single Organ Vasculitis

 • Cutaneous (leukocytoclastic) small vessel vasculitis

 • Cutaneous arteritis

 • Primary central nervous system vasculitis

 • Isolated aortitis

 • Others

6. Vasculitis associated with systemic disease

 • Lupus vasculitis

 • Rheumatoid vasculitis

 • Sarcoid vasculitis

 • Others

7. Vasculitis associated with probable etiology

 • Hepatitis C virus-associated cryoglobulinemic vasculitis

 • Hepatitis B virus-associated polyarteritis nodosa

 • Syphilis-associated vasculitis

 • Drug-associated immune complex vasculitis

 • Drug-associated ANCA-associated vasculitis

 • Cancer-associated vasculitis

 • Others