Vasculitis entities | |
---|---|
1. Large vessel vasculitis | |
• Giant Cell Arteritis • Takayasu Arteritis | |
2. Medium size vessel vasculitis | |
• Polyarteritis nodosa • Kawasaki disease | |
3. Small vessel vasculitis | |
ANCA-associated vasculitides | |
• Microscopic Polyangiitis • Granulomatosis with Polyangiitis • Eosinophilic Granulomatosis with Polyangiitis | |
Immune complex vasculitis | |
• Anti-GBM(glomerular basement membrane) disease • Cryoglobulinemic vasculitis • IgA vasculitis • Hypocomplementemic urticarial vasculitis (Anti-C1q vasculitis) | |
4. Variable Vessel Vasculitis | |
• Behcet’s disease • Cogan’s Syndrome | |
5. Single Organ Vasculitis | |
• Cutaneous (leukocytoclastic) small vessel vasculitis • Cutaneous arteritis • Primary central nervous system vasculitis • Isolated aortitis • Others | |
6. Vasculitis associated with systemic disease | |
• Lupus vasculitis • Rheumatoid vasculitis • Sarcoid vasculitis • Others | |
7. Vasculitis associated with probable etiology | |
• Hepatitis C virus-associated cryoglobulinemic vasculitis • Hepatitis B virus-associated polyarteritis nodosa • Syphilis-associated vasculitis • Drug-associated immune complex vasculitis • Drug-associated ANCA-associated vasculitis • Cancer-associated vasculitis • Others |