From: Adult onset Still’s disease in the elderly: a case-based literature review
Yamaguchi’s criteria [4] At least 5 criteria including 2 major criteria | Criteria met by our case | Fautrel’s criteria [5] 4 major or 3 major and 2 minor criteria | Criteria met by our case |
---|---|---|---|
Major: | Major: | ||
• Fever > 39 °C, lasting 1 week or longer • Arthralgia or arthritis, lasting 2 weeks or longer • Typical rash • Leukocytosis > 10,000/mm3 with > 80% polymorphonuclear cells | + + -a + | • Spiking fever ≥39 °C • Arthralgia • Transient erythema • Pharyngitis • Polymorphonuclear cells ≥80% • Glycosylated ferritin ≤20% | + + +a - + |
Minor: | Minor: | ||
• Sore throat • Lymphadenopathy • Hepatomegaly or splenomegaly • Abnormal liver function tests • Negative tests for antinuclear antibody and rheumatoid factor | - + - + −/+ | • Maculopapular rash • Leukocytosis ≥10,000/mm3 | + + |
Exclusion: | |||
• Infections • Malignancies (mainly malignant lymphoma) • Other rheumatic disease (mainly systemic vasculitides) | + + + |